Related liver fragment transplantation for type 1 glycogenosis: the first Russian experience The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology.
https://doi.org/10.23873/2074-0506-2011-0-2-3-24-28
Abstract
The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology.
About the Authors
A. V. Filin
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
A. V. Semenkov
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
N. A. Koroteyeva
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
A. Ya. Keligova
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
A. V. Metelin
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
E. F. Kim
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
D. S. Dzhamanchin
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
N. E. Khartukova
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
Yu. R. Kamalov
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
E. Yu. Kryzhanovskaya
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
V. A. Khovrin
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
T. N. Galyan
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
B. S. Kaganov
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
E. N. Kutyreva
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
A. I. Zubovich
Acad. B.V. Petrovsky Russian Surgery Research Center, Russian Academy of Medical Sciences; Research Institute of Nutrition, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
References
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Review
For citations:
Filin A.V., Semenkov A.V., Koroteyeva N.A., Keligova A.Ya., Metelin A.V., Kim E.F., Dzhamanchin D.S., Khartukova N.E., Kamalov Yu.R., Kryzhanovskaya E.Yu., Khovrin V.A., Galyan T.N., Kaganov B.S., Kutyreva E.N., Zubovich A.I. Related liver fragment transplantation for type 1 glycogenosis: the first Russian experience The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology. Transplantologiya. The Russian Journal of Transplantation. 2011;(2-3):24-28. (In Russ.) https://doi.org/10.23873/2074-0506-2011-0-2-3-24-28
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