Related liver fragment transplantation for type 1 glycogenosis: the first Russian experience The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology.
https://doi.org/10.23873/2074-0506-2011-0-2-3-24-28
Abstract
The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology.
About the Authors
A. V. FilinRussian Federation
A. V. Semenkov
Russian Federation
N. A. Koroteyeva
Russian Federation
A. Ya. Keligova
Russian Federation
A. V. Metelin
Russian Federation
E. F. Kim
Russian Federation
D. S. Dzhamanchin
Russian Federation
N. E. Khartukova
Russian Federation
Yu. R. Kamalov
Russian Federation
E. Yu. Kryzhanovskaya
Russian Federation
V. A. Khovrin
Russian Federation
T. N. Galyan
Russian Federation
B. S. Kaganov
Russian Federation
E. N. Kutyreva
Russian Federation
A. I. Zubovich
Russian Federation
References
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Review
For citations:
Filin A.V., Semenkov A.V., Koroteyeva N.A., Keligova A.Ya., Metelin A.V., Kim E.F., Dzhamanchin D.S., Khartukova N.E., Kamalov Yu.R., Kryzhanovskaya E.Yu., Khovrin V.A., Galyan T.N., Kaganov B.S., Kutyreva E.N., Zubovich A.I. Related liver fragment transplantation for type 1 glycogenosis: the first Russian experience The paper describes two clinical examples of successful related liver fragment transplantation for type 1 glycogenosis in a one-year-old boy and a 6-year-old girl. The given first successful clinical experience suggests that liver fragments for type 1 glycogenoses can be transplanted from live related donors and offers promise for the radical treatment of patients with this pathology. Transplantologiya. The Russian Journal of Transplantation. 2011;(2-3):24-28. (In Russ.) https://doi.org/10.23873/2074-0506-2011-0-2-3-24-28